Arrhythmogenic right ventricular dysplasia / cardiomyopathy (ARVD/C) is a rare familial disorder that may cause ventricular tachycardia and sudden cardiac death in young, apparently healthy individuals.

2024年3月20日 · Arrhythmogenic right ventricular cardiomyopathy (ARVC), a condition also known as arrhythmogenic right ventricular dysplasia, is part of the arrhythmogenic cardiomyopathies—constituting a genetic disorder of the myocardium that undergoes progressive fibrofatty infiltration, causing arrhythmias.

2024年5月31日 · Arrhythmogenic right ventricular dysplasia (ARVD) is a rare type of cardiomyopathy. It occurs when the muscle tissue in the right ventricle dies and is replaced with scar tissue. This disrupts the heart's electrical signals and causes arrhythmias. Symptoms include palpitations, fatigue, fainting and even cardiac arrest after physical activity.

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a form of heart disease that usually appears in adulthood. ARVC is a disorder of the myocardium, which is the muscular wall of the heart. This condition causes part of the myocardium to break down over time, increasing the risk of an abnormal heartbeat (arrhythmia) and sudden death.

Arrhythmogenic right ventricular cardiomyopathy (ARVC), also called arrhythmogenic right ventricular dysplasia (ARVD), is a genetic cardiac disorder affecting mainly the right ventricle and causing ventricular tachyarrhythmias and increased risk of sudden death.

2005年4月18日 · Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a primary cardiomyopathy that is often diagnosed after an individual presents with arrhythmia findings. Presenting manifestations include heart palpitations, syncope, or even sudden death.

ARVC is a genetic disease affecting the heart muscle, mainly in the right ventricle. It can cause abnormal heart rhythms, some of which can cause sudden death. It can also make the heart unable to pump enough blood.

2015年5月1日 · Enlargement of right ventricle and atrium. Cardiac echocardiogram. Early fibrosis and adipocytes infiltration.

2023年5月4日 · Right ventricular (RV) disease is predominant, but biventricular or left ventricular involvement may occur. ARVC prevalence is 1 in 2,500–5,000 persons. The second most frequent cause of SCD in persons under age 35 years, it causes up to 20% of cardiac-related deaths in this age group. Inheritance is largely autosomal dominant.

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is characterized by structural abnormalities, arrhythmias, and a spectrum of genetic and clinical manifestations. Clinically, ARVC is structurally distinguished by right ventricular dilation due to increased adiposity and fibrosis in the ventricular walls, and it manifests as cardiac arrhythmias ranging from non …

ARVC is an inherited disease that can cause abnormal and sometimes dangerous heart rhythms (arrhythmias) and changes in the heart muscle (cardiomyopathy). Because it is rare, ARVC and other types of ACM often go undetected. Our team …

2024年3月20日 · Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a genetic heart condition involving the breakdown of muscle tissue surrounding a part of your heart called the right ventricle....

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited heart condition in which the muscle of the right ventricle of the heart is replaced by fat and/or scar tissue. The condition often leads to the right ventricle losing the ability to pump blood. Individuals with ARVC often develop abnormal heart rhythms known as arrhythmias.

2017年1月5日 · Arrhythmogenic right ventricular cardiomyopathy (ARVC), also known as arrhythmogenic right ventricular dysplasia, is a heritable heart-muscle disorder that predominantly affects the right...

2001年12月1日 · Arrythmogenic right ventricular (RV) cardiomyopathy (ARVC) is a cardiomyopathy characterized pathologically by fibrofatty replacement primarily of the RV and clinically by life-threatening ventricular arrhythmias in apparently healthy young people.

What is Arrhythmogenic cardiomyopathy (ACM)? ACM is a genetic heart muscle condition which affects the right ventricle, left ventricle, or both. ACM has been referred to in the past as Arrhythmogenic Right Ventricular Cardiomyopathy as it was initially thought that it exclusively affected this pumping chamber of the heart.

2022年7月6日 · What is arrhythmogenic right ventricular cardiomyopathy (ARVC)? It is most common in people younger than 35 years of age, but it can happen at any age. The heart has 4 sections called chambers. The right ventricle is one of the lower chambers. If you have ARVC, a genetic defect causes muscle cells in your ventricle wall to die.

Arrhythmogenic right ventricular dysplasia (ARVD) is a rare genetic condition of the myocardium, with a significantly high risk of sudden death. Recent genetic research and improved understanding of the pathophysiology tend to change the ARVD ...

Arrhythmogenic Right Ventricular Cardiomyopathy or Dysplasia (ARVC or ARVD) is an inherited heart disorder that is characterized by the gradual replacement of the right heart muscle with fatty tissue.

2021年5月1日 · Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a genetic disease that involves a defect in the cells that hold the heart muscle together. Over time, the damaged cells are replaced by scar tissue and fat deposits.

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a myocardial disease, often familial, that is characterised pathologically by fibrofatty replacement of the right ventricular myocardium, and clinically by ventricular arrhythmias of right ventricular origin which may lead to sudden death, mostly in young people and athletes. 1-5 The term...

Arrhythmogenic right ventricular cardiomyopathy (ARVC), formerly called "arrhythmogenic right ventricular dysplasia" (ARVD), is the best characterized of the ACMs in relation to diagnosis, treatment and outcomes.

Background: The best approach for ablating ventricular tachycardia (VT) targeting right ventricular free wall (RVFW) aneurysms in arrhythmogenic right ventricular cardiomyopathy (ARVC) remains undefined. Objectives: We aimed to describe the technical approach, safety and long-term efficacy of endocardial ablation of VT originating from RVFW aneurysms in ARVC patients.

2025年2月10日 · Right ventricular failure contributes to the morbidity and mortality of acute myocardial function, massive pulmonary embolism, and chronic pulmonary hypertension. Understanding how the normal physiology of the RV is disrupted is integral to managing patients who present with RV decompensation. Therapeutic advances in mechanical circulatory …

2019年10月29日 · Electrocardiogram (ECG)-specific findings may suggest RV versus LV disease. Low QRS voltage in the limb leads is a marker of LV involvement. The diagnosis of ARVC in pediatric patients is difficult due to the low prevalence of phenotypic disease.

6 天之前 · For patients undergoing LBBAP, a fixed-curve sheath (C315HIS, Medtronic) was introduced to the right ventricle under the fluoroscopic right anterior oblique 30°, advancing a pacing lead with fixed helix (Selectsecure model 3830, 69 cm, Medtronic) into the ventricular septum from the right side of V-V septum towards the left bundle branch area.

2025年2月11日 · Nonischemic cardiomyopathy was the most common underlying structural heart disorder (approximately 74% of 121 patients reported by Vaseghi et al. ) ... and had significant left or right ventricular dysfunction (mean LV ejection fraction 30 ± 13% in Vaseghi et al.) . The majority of studies reporting on these patients included cohorts in which ...

2 天之前 · BACKGROUND: In patients with hypertrophic cardiomyopathy, the prognostic value of myocardial T1 and extracellular volume fraction for adverse cardiovascular events has not been well defined. METHODS: A total of 663 consecutive participants with hypertrophic cardiomyopathy who underwent 3T cardiovascular magnetic resonance were recruited. The follow-up end …

5 天之前 · A left ventricular ring-like late gadolinium pattern in a 27-year-old young male with desmin cardiomyopathy Get access. ... Brain diffusion-weighted imaging showed acute ischaemic stroke in the right frontal. Echocardiogram (Panel B) showed biatrial enlargement and impaired right ventricular systolic function (TAPSE 12 mm), with a left ...